This is an autosomal dominant inherited tendency to multiple, small, flesh- colored, translucent Tumours from childhood, mainly on the face. There is a risk of basal cell carcinoma developing in the lesions. The condition has been mapped to chromosome 9p21, close to D9S126 (Harada et al. 1996; Clarke et al. 2002). The condition is caused by mutations in the CYLD gene, thus allelic with Brooke–Spiegler syndrome (Saggar et al. 2008). Brooke–Spiegler syndrome is an autosomal dominant syndrome characterized by multiple cylindromas and trichoepitheliomas.