OCULAR CHORISTOMA TUMOURS
Ocular choristomas are congenital lesions, which are deposits of normal tissue in an abnormal location. They are the most common epibulbar and orbital Tumours in children, with an incidence of about 1 per 5,000 (Mansour et al. 1989). Dermoid and epidermoid cysts are both included in this group.
Ocular choristomas may be associated with Goldenhar syndrome (hemifacial microsomia) or epidermal nevus syndrome. In the latter disorder, choristomas are frequently bilateral and extensive. Goldenhar syndrome is usually sporadic but in rare cases can be familial (Tasse et al. 2007). Familial choristoma with dominant inheritance not associated with Goldenhar syndrome occurs rarely (Mansour et al. 1989).